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Modeling Human TBX5 Haploinsufficiency Predicts Regulatory Networks for Congenital Heart Disease

Irfan S. Kathiriya, Kavitha S. Rao, Giovanni Iacono, W. Patrick Devine, Andrew P. Blair, Swetansu K. Hota, Michael H. Lai, Bayardo I. Garay, Reuben Thomas, Henry Gong, Lauren K. Wasson, Piyush Goyal, Tatyana Sukonnik, Kevin Hu, Güneş Akgün, Laure D. Bernard, Brynn N. Akerberg, Fei Gu, Kai Li, Matthew L Speir, Maximilian Haeussler, William T. Pu, Joshua M. Stuart, Christine E. Seidman, J G Seidman, Holger Heyn, Benoit G. Bruneau

2020Developmental Cell130 citationsDOIOpen Access PDF

Topics & Concepts

HaploinsufficiencyBiologyInduced pluripotent stem cellGene regulatory networkMEF2CTranscription factorTranscriptomeHeart developmentEnhancerRegulation of gene expressionHeart diseaseGeneGeneticsCell biologyComputational biologyGene expressionPhenotypeEmbryonic stem cellInternal medicineMedicineCongenital heart defects researchCRISPR and Genetic EngineeringCongenital Heart Disease Studies
Modeling Human TBX5 Haploinsufficiency Predicts Regulatory Networks for Congenital Heart Disease | Litcius