Litcius/Paper detail

Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management

Cormac McCarthy, Nishant Gupta, Simon R. Johnson, Jane Yu, Francis X. McCormack

2021The Lancet Respiratory Medicine199 citationsDOI

Topics & Concepts

LymphangioleiomyomatosisMedicineTuberous sclerosisSirolimusPI3K/AKT/mTOR pathwayTSC1PathologyDiscovery and development of mTOR inhibitorsBioinformaticsCancer researchInternal medicineSignal transductionBiologyBiochemistryTuberous Sclerosis Complex ResearchEosinophilic Disorders and SyndromesInterstitial Lung Diseases and Idiopathic Pulmonary Fibrosis