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Anomalous peroxidase activity of cytochrome c is the primary pathogenic target in Barth syndrome

Valerian E. Kagan, Yulia Y. Tyurina, Karolina Mikulska‐Ruminska, Deena Damschroder, Eduardo Vieira Neto, Alessia Lasorsa, Alexander A. Kapralov, Vladimir A. Tyurin, Andrew A. Amoscato, Svetlana N. Samovich, Austin B. Souryavong, Haider H. Dar, Abu Ramim, Zhuqing Liang, Pablo Lazcano, Jiajia Ji, Michael W. Schmidtke, Kirill Kiselyov, Aybike Korkmaz, G. K. Vladimirov, Margarita A. Artyukhova, Pushpa Rampratap, Laura Cole, Ammanamanchi Niyatie, Emma-Kate Baker, Jim Peterson, Grant M. Hatch, Jeffrey Atkinson, Jerry Vockley, Bernhard Kühn, Robert Wessells, Patrick C.A. van der Wel, İvet Bahar, Hülya Bayır, Miriam L. Greenberg

2023Nature Metabolism23 citationsDOIOpen Access PDF

Topics & Concepts

CardiolipinPeroxidaseBiochemistryChemistryCytochrome cLipid peroxidationMitochondrionPhospholipidOxidative stressEnzymeMembraneMitochondrial Function and PathologyPhotosynthetic Processes and MechanismsATP Synthase and ATPases Research
Anomalous peroxidase activity of cytochrome c is the primary pathogenic target in Barth syndrome | Litcius