Urinary bicarbonate and metabolic alkalosis during exacerbations in cystic fibrosis
Giulia Spoletini, G. Fitch, Lindsey Gillgrass, C. Etherington, I. Clifton, D. Peckham
Abstract
Pseudo-Bartter syndrome (PBS) is characterised by hypokalaemic, hyponatraemic and hypochloraemic metabolic alkalosis in the absence of renal tubules pathology; it is a well-recognised complication of cystic fibrosis (CF), in the context of dehydration and acute illness [1–7]. The aetiology of increased serum bicarbonate and metabolic alkalosis in CF is complex and appears to be driven, at least in part, by renal tubular CFTR dysfunction <https://bit.ly/3NFPkUu>
Topics & Concepts
MedicineCystic fibrosisMetabolic alkalosisBicarbonateUrinary systemAlkalosisInternal medicineEtiologySodium bicarbonateUrologyGastroenterologyEndocrinologyAcidosisPhysical chemistryChemistryCystic Fibrosis Research AdvancesNeonatal Respiratory Health ResearchTracheal and airway disorders