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Metabolic reprogramming in a slowly developing orthologous model of polycystic kidney disease

Katharina Hopp, Emily K. Kleczko, Berenice Y. Gitomer, Michel Chonchol, Jost Klawitter, Jost Klawitter, Uwe Christians, Jelena Klawitter, Jelena Klawitter

2022American Journal of Physiology-Renal Physiology35 citationsDOIOpen Access PDF

Abstract

This report delineates the evolution of metabolic changes occurring during autosomal dominant polycystic kidney disease (ADPKD) progression. Using an orthologous model, we performed kidney metabolomics and confirmed dysregulation of metabolic pathways previously found altered in nonorthologous or rapidly-progressive PKD models. Importantly, we identified novel alterations, including augmentation of kynurenines, polyamines, and indoles, suggesting increased inflammation and microbial dysbiosis that provide insights into PKD pathomechanisms and may prove helpful for diagnosing, monitoring, and treating ADPKD.

Topics & Concepts

Autosomal dominant polycystic kidney diseasePolycystic kidney diseasePKD1BiologyMetabolomicsDysbiosisDiseaseReprogrammingKidney diseaseInflammationKidneyBioinformaticsMicrobiomeGeneticsMedicineEndocrinologyInternal medicineImmunologyGeneGenetic and Kidney Cyst DiseasesBiomedical Research and PathophysiologyEpigenetics and DNA Methylation
Metabolic reprogramming in a slowly developing orthologous model of polycystic kidney disease | Litcius