Impairment of mitochondrial oxidative phosphorylation in skin fibroblasts of SALS and FALS patients is rescued by in vitro treatment with ROS scavengers
Grażyna Dębska–Vielhaber, Irina Miller, Viktoriya Peeva, Werner Zuschratter, Jarosław Walczak, Stefanie Schreiber, Susanne Petri, Judith Machts, Susanne Vogt, Joanna Szczepanowska, Frank N. Gellerich, Andreas Hermann, Stefan Vielhaber, Wolfram S. Kunz
Topics & Concepts
TARDBPSOD1Amyotrophic lateral sclerosisC9orf72MitochondrionBiologyOxidative phosphorylationOxidative stressMitochondrial DNAMitochondrial diseaseCancer researchMolecular biologyGeneticsGenePathologySuperoxide dismutaseDiseaseMedicineTrinucleotide repeat expansionBiochemistryAlleleAmyotrophic Lateral Sclerosis ResearchNeurogenetic and Muscular Disorders ResearchGenetic Neurodegenerative Diseases