Successful treatment with ustekinumab in CARD14‐associated papulosquamous eruption in a Brazilian child
Ana Elisa Kiszewski, Hiram Larangeira de Almeida
Abstract
CARD14-associated papulosquamous eruption (CAPE) was proposed in 2018 to describe the clinical features of psoriasis and pityriasis rubra pilaris with CARD 14 mutations. We report a 5-month-old female infant who developed CAPE-associated erythroderma. Although she did not respond to conventional therapies, she responded well to ustekinumab treatment at the age of 4 years.
Topics & Concepts
Pityriasis rubra pilarisMedicineUstekinumabDermatologyErythrodermaPsoriasisPediatricsDiseaseInternal medicineInfliximabCutaneous lymphoproliferative disorders researchFungal Infections and StudiesImmunodeficiency and Autoimmune Disorders