Independent mechanisms of inflammation and myeloid bias in VEXAS syndrome
Varun Narendra, Tandrila Das, Linsey J. Wierciszewski, Rebecca J. Londoner, Joshua Morrison, Pia Martindale, Tom Devine, Kevin Chen, M. Trombetta, Yuzuka Kanno, Alejandro E. Casiano, Elisa de Stanchina, Caleb A. Lareau, Scott W. Lowe, Alexander D. Gitlin
Topics & Concepts
InflammationPathogenesisHaematopoiesisMyeloidBiologyImmunologyCancer researchMutationSomatic cellProgenitor cellStem cellProgrammed cell deathInnate immune systemGermline mutationMedicineProinflammatory cytokineDiseaseNecroptosisTumor necrosis factor alphaMacrophageProto-Oncogene Proteins c-kitCell biologyPhenotypeApoptosisOtitis Media and Relapsing PolychondritisOsteomyelitis and Bone Disorders ResearchSpondyloarthritis Studies and Treatments