Epidemiology and geographic clustering of Erdheim-Chester disease in Italy and France
Francesco Peyronel, Julien Haroche, Corrado Campochiaro, Francesco Pegoraro, Zahir Amoura, Alessandro Tomelleri, Martina Mazzariol, Matthias Papo, Giulio Cavalli, Giuseppe Daniele Benigno, Paride Fenaroli, Chrysanthos Grigoratos, Maria Cecilia Mengoli, Arturo Bonometti, Emilio Berti, Gustavo Savino, Mauro Cives, Iria Neri, Gaetano Pacinella, Antonino Tuttolomondo, Massimo Marano, Francesco Muratore, Andreina Manfredi, Alessandro Broccoli, Pier Luigi Zinzani, Biagio Didona, Chiara Massaccesi, Andrea Buono, Enrico Ammirati, Vito Di Lernia, Lorenzo Dagna, Augusto Vaglio, Fleur Cohen‐Aubart
Abstract
This geoepidemiological study, performed in Italy and France, shows that Erdheim-Chester disease is increasingly diagnosed and cases cluster in specific geographic areas, namely southern Italy and central France. Disease frequency inversely correlates with the Human Development Index.