A novel unbiased method reveals progressive podocyte globotriaosylceramide accumulation and loss with age in females with Fabry disease
Behzad Najafian, Aurelio Silvestroni, Alexey Sokolovskiy, Camilla Tøndel, Einar Svarstad, Bogdan Obrișcă, Gener Ismail, Myrl Holida, Michael Mauer
Topics & Concepts
PodocyteGlobotriaosylceramideFabry diseaseProteinuriaUrologyMedicineEndocrinologyInternal medicineDiseaseKidneyLysosomal Storage Disorders ResearchRenal Diseases and GlomerulopathiesComplement system in diseases