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A novel unbiased method reveals progressive podocyte globotriaosylceramide accumulation and loss with age in females with Fabry disease

Behzad Najafian, Aurelio Silvestroni, Alexey Sokolovskiy, Camilla Tøndel, Einar Svarstad, Bogdan Obrișcă, Gener Ismail, Myrl Holida, Michael Mauer

2022Kidney International16 citationsDOIOpen Access PDF

Topics & Concepts

PodocyteGlobotriaosylceramideFabry diseaseProteinuriaUrologyMedicineEndocrinologyInternal medicineDiseaseKidneyLysosomal Storage Disorders ResearchRenal Diseases and GlomerulopathiesComplement system in diseases
A novel unbiased method reveals progressive podocyte globotriaosylceramide accumulation and loss with age in females with Fabry disease | Litcius