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Trametinib for Refractory Chylous Effusions and Systemic Complications in Children with Noonan Syndrome

Taizo A. Nakano, Alexander W. Rankin, Aparna Annam, Ann M. Kulungowski, Leslie McCallen, Lauren R. S. Hill, Kathryn C. Chatfield

2022The Journal of Pediatrics45 citationsDOIOpen Access PDF

Topics & Concepts

MedicineNoonan syndromeTrametinibMEK inhibitorInternal medicineDosingMAPK/ERK pathwayOncologyKinaseBiologyCell biologyProtein Tyrosine PhosphatasesPI3K/AKT/mTOR signaling in cancerDermatological and Skeletal Disorders
Trametinib for Refractory Chylous Effusions and Systemic Complications in Children with Noonan Syndrome | Litcius