Litcius/Paper detail

Anti-C5 antibody treatment for delayed hemolytic transfusion reactions in sickle cell disease

Aline Floch, Alexandre Morel, Fabian Zanchetta-Balint, Catherine Cordonnier-Jourdin, Slimane Allali, Maximilien Grall, Ghislaine Ithier, Benjamin Carpentier, Sadaf Pakdaman, Jean‐Claude Merle, Radjiv Goulabchand, Tackwa Khalifeh, Ana Berceanu, Cécile Helmer, Christelle Chantalat‐Auger, Véronique Frémeaux-Bacchi, Marc Michel, Mariane de Montalembert, Armand Mekontso Dessap, France Pirenne, Anoosha Habibi, Pablo Bartolucci

2020Haematologica29 citationsDOIOpen Access PDF

Abstract

Continuous variables are expressed as means one standard deviation (SD) or medians (MD, [interquartile range]), depending on whether they are normally or asymmetrically distributed. Categorical variables are expressed as numbers (%). For comparison with the largest published delayed hemolytic transfusion reaction (DHTR) series, the data in column 2 are reprinted from Habibi et al.1 with permission. The patients of our series, who received anti-C5 antibody, had very severe DHTR with hyperhemolysis (P-values in column 3 compare our patients with those of the historical series). *Six patients had not even been discharged, due to the severity of their DHTR, **All patients in both series also received supportive vaso-occlusive crisis (VOC) treatment, hydration, oxygenation, and analgesia. Values were converted to g/L (from g/dL in Habibi et al.). Delta hemoglobin ( Hb) is the difference between the highest and lowest values available post-transfusion. F

Topics & Concepts

MedicineAntibodyImmunologyHemolytic anemiaIsoantibodiesDiseaseBlood transfusionInternal medicineBlood groups and transfusionHemoglobinopathies and Related DisordersErythrocyte Function and Pathophysiology