Respiratory decline in adult patients with Becker muscular dystrophy: A longitudinal study
Bram De Wel, Sofie Willaert, Aleksandra Nadaj‐Pakleza, Anne-Catherine Aubé-Nathier, Dries Testelmans, Bertien Buyse, Kristl G. Claeys
Topics & Concepts
MedicineVital capacityMuscular dystrophyDuchenne muscular dystrophyPulmonary function testingBody mass indexPediatricsNatural historyRespiratory systemInternal medicinePhysical therapyLungLung functionDiffusing capacityMuscle Physiology and DisordersNeurogenetic and Muscular Disorders ResearchIon channel regulation and function