Epidermolysis Bullosa Pruriginosa successfully treated with concomitant topical and systemic agents
Sandra Ferreira, Alexandra Azevedo, Glória Velho, Madalena Sanches, Manuela Selores
Abstract
Epidermolysis bullosa pruriginosa, a genetic mechanobullous disease, manifests at birth or late in life and is characterised by intense pruritus, resulting in lichenified or nodular prurigo-like lesions and scarring most prominent on the shins. Treatment is unsatisfactory. We report a patient treated with success using a combination of topical and systemic agents.
Topics & Concepts
MedicineEpidermolysis bullosaDermatologyConcomitantSystemic diseaseDiseaseSurgeryPathologySkin and Cellular Biology ResearchAutoimmune Bullous Skin DiseasesNail Diseases and Treatments