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N-acetylcysteine amide ameliorates mitochondrial dysfunction and reduces oxidative stress in hiPSC-derived dopaminergic neurons with POLG mutation

Kristina Xiao Liang, Guro Helén Vatne, Cecilie Katrin Kristiansen, Oleksandr Ievglevskyi, Elena Kondratskaya, Joel C. Glover, Anbin Chen, Gareth J. Sullivan, Laurence A. Bindoff

2020Experimental Neurology32 citationsDOI

Topics & Concepts

BiologyMitochondrial DNAMitochondrionDopaminergicTFAMOxidative stressMitochondrial diseaseCell biologyNeuroscienceGeneticsDopamineEndocrinologyMitochondrial biogenesisGeneMitochondrial Function and PathologyGenetic Neurodegenerative DiseasesPluripotent Stem Cells Research
N-acetylcysteine amide ameliorates mitochondrial dysfunction and reduces oxidative stress in hiPSC-derived dopaminergic neurons with POLG mutation | Litcius