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Trehalose Ameliorates Seizure Susceptibility in Lafora Disease Mouse Models by Suppressing Neuroinflammation and Endoplasmic Reticulum Stress

Priyanka Sinha, Bhupender Verma, Subramaniam Ganesh

2020Molecular Neurobiology59 citationsDOI

Topics & Concepts

Lafora diseaseGliosisNeuroinflammationProgressive myoclonus epilepsyEndoplasmic reticulumUnfolded protein responseAutophagyAstrogliosisBiologyProteostasisNeuropathologyNeurodegenerationCell biologyEpilepsyImmunologyEndocrinologyNeuroscienceMedicinePathologyGeneticsCentral nervous systemDiseaseInflammationPhosphataseApoptosisPhosphorylationGlycogen Storage Diseases and MyoclonusLysosomal Storage Disorders ResearchGenetics and Neurodevelopmental Disorders
Trehalose Ameliorates Seizure Susceptibility in Lafora Disease Mouse Models by Suppressing Neuroinflammation and Endoplasmic Reticulum Stress | Litcius