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Characterization of <i>ANGPT2</i> mutations associated with primary lymphedema

Veli‐Matti Leppänen, Pascal Brouillard, Emilia A. Korhonen, Tuomas Sipilä, Sawan Kumar Jha, Nicole Revençu, Veerle Labarque, Elodie Fastré, Matthieu J. Schlögel, Marie Ravoet, Amihood Singer, C. Luzzatto, Donatella Angelone, Giovanni Crichiutti, Angela D’Elia, Jaakko Kuurne, Harri Elamaa, Gou Young Koh, Pipsa Saharinen, Miikka Vikkula, Kari Alitalo

2020Science Translational Medicine48 citationsDOIOpen Access PDF

Abstract

Loss-of-function mutations in the TIE2-ligand angiopoietin 2 are associated with primary lymphedema in humans.

Topics & Concepts

Angiopoietin receptorMissense mutationBiologyLymphatic systemLymphedemaCancer researchLymphatic EndotheliumLymphangiogenesisCell biologyMutantMutationImmunologyGeneticsGeneAngiogenesisCancerBreast cancerMetastasisLymphatic System and DiseasesAngiogenesis and VEGF in CancerCoagulation, Bradykinin, Polyphosphates, and Angioedema
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