Refractory Minimal Change Disease and Focal Segmental Glomerular Sclerosis Treated With Anakinra
Andrea Angeletti, Alberto Magnasco, AntonellaTrivelli, Ludovica M. Degl’Innocenti, Giorgio Piaggio, Francesca Lugani, Gianluca Caridi, Enrico Verrina, Paolo Cravedi, Gian Marco Ghiggeri
Abstract
Idiopathic nephrotic syndrome (NS) is the most common cause of proteinuria in children and young adults. Minimal lesion with fusion of slit-diaphragm is the pathologic substrate in most cases,1 whereas focal segmental glomerular sclerosis (FSGS) often corresponds to drug-unresponsive forms that are at higher risk to develop progressive kidney failure.S1
Topics & Concepts
MedicineNephrotic syndromeAnakinraProteinuriaRefractory (planetary science)Minimal change diseaseFocal segmental glomerulosclerosisLesionSlit diaphragmDiaphragm (acoustics)Internal medicinePathologyDiseaseKidneyPodocyteAcousticsAstrobiologyPhysicsLoudspeakerRenal Diseases and GlomerulopathiesAmyloidosis: Diagnosis, Treatment, OutcomesSystemic Sclerosis and Related Diseases