Litcius/Paper detail

Treatment of necrobiosis lipoidica with combination Janus kinase inhibition and intralesional corticosteroid

William Damsky, Katelyn Singh, Anjela Galan, Brett King

2020JAAD Case Reports30 citationsDOIOpen Access PDF

Abstract

Necrobiosis lipoidica (NL) is an idiopathic granulomatous disorder that causes plaques on the lower part of the legs that commonly ulcerate. Histologically, NL shows palisaded granulomatous inflammation horizontally layered within degenerated collagen and an associated lymphoplasmacytic infiltrate. Little is known about the molecular pathogenesis of NL, and no reliably effective therapies exist.

Topics & Concepts

Necrobiosis lipoidicaMedicinePathogenesisPathologyJanus kinaseInflammationGranulomatous inflammationPyoderma gangrenosumDermatologyImmunologyDiabetes mellitusCytokineEndocrinologyDiseaseSkin Diseases and DiabetesInflammatory Myopathies and DermatomyositisDermatological and Skeletal Disorders