Left ventricular radial strain impairment precedes hypertrophy in Anderson–Fabry disease
Letìzia Spinelli, Giuseppe Giugliano, Massimo Imbriaco, Giovanni Esposito, Carmela Nappi, Eleonora Riccio, Andrea Ponsiglione, Antonio Pisani, Alberto Cuocolo, Bruno Trimarco
Topics & Concepts
CardiologyInternal medicineEjection fractionMedicineFabry diseaseConcentric hypertrophyMuscle hypertrophyRadial stressLeft ventricular hypertrophySpeckle tracking echocardiographyDiastolePopulationFibrosisDiseaseHeart failureBlood pressureVelocity vectorEnvironmental healthEngineeringAerospace engineeringCardiovascular Function and Risk FactorsLysosomal Storage Disorders ResearchCardiomyopathy and Myosin Studies