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Progressive Disease With Low Survival in Adult Patients With Pulmonary Fibrosis Carrying Surfactant-Related Gene Mutations

Dymph Klay, Jan C. Grutters, Joanne J. van der Vis, Mark G. J. P. Platenburg, Johannes C. Kelder, Ellen Tromp, Coline H.M. van Moorsel

2022CHEST Journal24 citationsDOIOpen Access PDF

Topics & Concepts

MedicineInterstitial lung diseaseInternal medicinePulmonary function testingIdiopathic pulmonary fibrosisPulmonary fibrosisProgressive diseaseGastroenterologySurfactant protein CLungGene mutationDiffusing capacityCohortVital capacityMutationDiseaseLung functionGeneBiologyGeneticsInterstitial Lung Diseases and Idiopathic Pulmonary FibrosisNeonatal Respiratory Health ResearchCystic Fibrosis Research Advances
Progressive Disease With Low Survival in Adult Patients With Pulmonary Fibrosis Carrying Surfactant-Related Gene Mutations | Litcius