Litcius/Paper detail

FCGR3B polymorphism predicts relapse risk in eosinophilic granulomatosis with polyangiitis

Federico Alberici, Francesco Bonatti, Alessia Adorni, Giulia Daminelli, Renato Alberto Sinico, Gina Gregorini, Chiara Marvisi, Paride Fenaroli, Francesco Peyronel, Federica Maritati, Alessandra Palmisano, Maria Letizia Urban, Antonio Percesepe, Giacomo Emmi, Davide Martorana, Augusto Vaglio

2020Lara D. Veeken16 citationsDOI

Abstract

Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare disease included in the spectrum of ANCA-associated vasculitis, although ANCA (usually anti-MPO, MPO ANCA) are positive in only ∼40% of patients. EGPA almost invariably shows eosinophilia, asthma and rhinosinusitis. Other manifestations tend to segregate in two main subsets defined on ANCA status, with ANCA-positive patients more commonly showing vasculitic manifestations [1]. The genetic background of EGPA is complex: ANCA-positive EGPA is associated with HLA-DQ (similar to MPO ANCA-associated vasculitis), while the ANCA-negative subgroup...

Topics & Concepts

MedicineFamily medicineInternal medicineEosinophilic Disorders and SyndromesEosinophilic EsophagitisVasculitis and related conditions