Effects of elexacaftor/tezacaftor/ivacaftor therapy in children with cystic fibrosis – a comprehensive assessment using lung clearance index, spirometry, and functional and structural lung MRI
Carmen Streibel, Corin Willers, Orso Pusterla, Grzegorz Bauman, Enno Stranzinger, Ben Brabandt, Oliver Bieri, Marion Curdy, Marina Bullo, Bettina Frauchiger, Insa Korten, Linn Krüger, Carmen Casaulta, Félix Ratjen, Philipp Latzin, Elisabeth Kieninger
Topics & Concepts
IvacaftorMedicineSpirometryCystic fibrosisVentilation (architecture)LungLung functionInternal medicineCystic fibrosis transmembrane conductance regulatorCardiologyNuclear medicineMechanical engineeringEngineeringAsthmaCystic Fibrosis Research AdvancesDelphi Technique in ResearchChronic Obstructive Pulmonary Disease (COPD) Research