Treatment with a triazole inhibitor of the mitochondrial permeability transition pore fully corrects the pathology of sapje zebrafish lacking dystrophin
A. Stocco, Natalia Smolina, Patrizia Sabatelli, Justina Šileikytė, Edoardo Artusi, Vincent Mouly, Michael S. Cohen, Michael Forte, Marco Schiavone, Paolo Bernardi
Topics & Concepts
ZebrafishDystrophinMitochondrial permeability transition poreMyogenesisDuchenne muscular dystrophyIn vivoMitochondrionCell biologyBiologyMyocyteChemistryPharmacologyApoptosisBiochemistryProgrammed cell deathGeneticsGeneMuscle Physiology and DisordersAdipose Tissue and MetabolismMitochondrial Function and Pathology