Enforced dimerization between XBP1s and ATF6f enhances the protective effects of the UPR in models of neurodegeneration
René L. Vidal, Denisse Sepúlveda, Paulina Troncoso-Escudero, Paula García-Huerta, Constanza González, Lars Plate, Carolina Jerez, José Cánovas, Claudia A. Rivera, Valentina Castillo, Marisol Cisternas, Sirley Leal, Alexis Martínez, Julia M. D. Grandjean, Sonia Donzelli, Hilal A. Lashuel, Alberto J. M. Martín, Verónica Latapiat, Soledad Matus, S. Pablo Sardi, R. Luke Wiseman, Claudio Hetz
Topics & Concepts
ProteostasisUnfolded protein responseATF6NeurodegenerationBiologyCell biologyXBP1HuntingtinATF4NeuroprotectionEndoplasmic reticulumTranscription factorGeneMutantNeuroscienceGeneticsDiseaseRNAMedicinePathologyRNA splicingEndoplasmic Reticulum Stress and DiseaseAutophagy in Disease and TherapyTransgenic Plants and Applications