Litcius/Paper detail

Genetically and clinically confirmed atypical cerebrotendinous xanthomatosis with normal cholestanol and marked elevations of bile acid precursors and bile alcohols

Andrea E. DeBarber, Ernst J. Schaefer, Jenny Do, Joseph W. Ray, Austin Larson, Samantha Redder, Maya Fowler, P. Barton Duell

2024Journal of clinical lipidology14 citationsDOI

Topics & Concepts

Cerebrotendinous XanthomatosisCholestanolMedicineBile acidInternal medicineGastroenterologySterolCholesterolCholesterol and Lipid MetabolismPeroxisome Proliferator-Activated ReceptorsFatty Acid Research and Health