VEXAS syndrome: a comprehensive review of pathogenesis, clinical spectrum, and therapeutic strategies
Emma M. Groarke, Benjamin A. Turturice, Bhavisha A. Patel, Kaitlin A Quinn, Alice Fike, Peter C. Grayson
Topics & Concepts
MedicineSomatic cellHaematopoiesisInflammationDiseaseImmunologyBone marrowBioinformaticsStem cellTherapeutic approachSystemic inflammationInternal medicineGlucocorticoidOncologyLeukemiaEpigeneticsGene mutationGermline mutationAge of onsetGenetic enhancementAdult-onset Still's diseaseCellHematopoietic stem cellPathogenesisOtitis Media and Relapsing PolychondritisOsteomyelitis and Bone Disorders ResearchVascular Anomalies and Treatments