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Dysregulated innate immune signaling cooperates with RUNX1 mutations to transform an MDS-like disease to AML

Laura Barreyro, Avery Sampson, Kathleen Hueneman, Kwangmin Choi, Susanne Christie, Vighnesh Ramesh, Michael A. Wyder, Dehua Wang, Mario Pujato, Kenneth D. Greis, Gang Huang, Daniel T Starczynowski

2024iScience15 citationsDOIOpen Access PDF

Abstract

HSPCs, highlighting the necessity of TRAF6-dependent cell-intrinsic innate immune signaling in initiating and maintaining AML. These findings underscore the critical role of dysregulated cell-intrinsic innate immune signaling in driving preleukemic cells toward AML progression.

Topics & Concepts

Innate immune systemRUNX1Immune systemMyeloidImmunologySignal transductionInnate lymphoid cellBiologyDiseaseCancer researchCell biologyGeneticsMedicineTranscription factorGeneInternal medicineImmune cells in cancerAcute Myeloid Leukemia Researchinterferon and immune responses