The structure of a calsequestrin filament reveals mechanisms of familial arrhythmia
Erron W. Titus, Fred Deiter, Chenxu Shi, Julianne Wojciak, Melvin M. Scheinman, Natalia Jura, Rahul C. Deo
Topics & Concepts
CalsequestrinCatecholaminergic polymorphic ventricular tachycardiaProtein filamentCell biologyMutationBiologyBiophysicsChemistryGeneticsRyanodine receptor 2IntracellularGeneRyanodine receptorIon channel regulation and functionCardiac electrophysiology and arrhythmiasCardiomyopathy and Myosin Studies